Primary Sjogren’s syndrome presents as recurrent meningoencephalitis
Rare presentation of Sjogren's Syndrome
Abstract
Primary Sjogren’s syndrome is an autoimmune disease mostly affecting middle-aged females. It usually involves the exocrine glands system resulting in dryness of the mouth and eyes. It rarely involves the Central nervous system. Here we present a case of Sjogren’s syndrome with a rare presentation at an unusual age. An 80 years old patient who presented with 3 episodes of recurrent aseptic meningitis in a year, was diagnosed with primary Sjogren’s syndrome after extensive workup. She responded well to immunomodulatory treatment. Clinicians should consider the rare presentation and age of autoimmune diseases when facing the challenging clinical situation.
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